目的 探讨婴幼儿法洛四联症根治术的手术治疗效果。 方法 回顾性分析2008年9月至2009年6月59例在湖南省儿童医院行婴幼儿法洛四联症根治术59例患者的临床资料。其中男37例，女22例；年龄0.5～3.0 （1.9±0.4） 岁。分析其早期和中期效果。 结果 治愈率为94.9% （56/59），死亡率为5.1% （3/59），术后并发症发生率为16.9% （10/59）。体外循环时间为（105.2±9.5） min，主动脉阻断时间为（72.8±5.1） min，术后呼吸机辅助呼吸时间为（42.6±8.2） h，住院时间为（17.9±1.7） d。随访2年后，所有生存患儿的远期疗效均良好，紫绀消失，活动量明显增加。 结论 婴幼儿法洛四联症根治术近远期疗效良好，值得在临床上推广与应用。
Citation：
曾德斌,刘平波,阳广贤,杨威,易立文. 婴幼儿法洛四联症的手术治疗效果分析. Chinese Journal of Clinical Thoracic and Cardiovascular Surgery, 2013, 20(5): 596-597. doi: 10.7507/1007-4848.20130181
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- 1. Bharati AH， Naware A， Merchant SA. Absent pulmonary valvesyndrome with tetralogy of Fallot and associated dextrocardia detectedat an early gestational age of 26 weeks. Indian J Radiol Imaging， 2008， 18 （4）：352-354.
- 2. Abd El Rahman MY， Hui W， Dsebissowa F， et al. Quantitative analysis of paradoxical interventricular septal motion following corre-ctive surgery of tetralogy of fallot. Pediatr Cardiol， 2005， 26 （4）：379-384.
- 3. Patel CR， Agamanolis DP， Stewart JW. Prenatal diagnosis of tetralogyof Fallot with obstructed supracardiac totally anomalous pulmonary venous connection. Cardiol Young， 2005， 15 （6）：656-659.
- 4. 丁文祥， 苏肇伉， 主编. 小儿心脏外科学. 山东：山东技术出版社， 2000. 370.
- 5. Takahashi S， Oishi Y， Ito N， et al. Evaluating mortality and disease severity in congenital diaphragmatic hernia using the McGoon and pulmonary artery indices. J Pediatr Surg， 2009， 44 （11）：2101-2106.
- 6. Book WM， Parks WJ， Hopkins KL， et al. Electrocardiographicpredictors of right ventricular volume measured by magnetic resonanceimaging late after total repair of tetralogy of Fallot. Clin Cardiol， 1999， 22 （11）：740-746.
- 7. Mivelaz Y， Lim KI， Templeton C， et al. Review of the natural historyof tetralogy of Fallot with absent pulmonary valve syndrome：does prenatal diagnosis imply increased risk ? Ultrsound Obstet Gynecol， 2010， （S1）：156.
- 8. Sivakumar K， Krishnan P， Pieris R， et al. Hybrid approach to surgicalcorrection of tetralogy of Fallot in all patients with functioning BlalockTaussig shunts. Catheter Cardiovasc Interv， 2007， 70 （2）：256-264.
- 9. Spivack E. Tetralogy of fallot：an overview， case report， and discu-ssion of dental implications. Spec Care Dentist， 2008， 21 （5）：172-175.
- 10. He GW. Current strategy of repair of tetralogy of Fallot in children and adults：emphasis on a new technique to create a monocusp-patch for Reconstruction of the right ventricular outflow tract. J Card Surg， 2008， 23 （6）：592-599.
- 11. Çetin İ， Tokel K， Varan B， et al. Evaluation of right ventricular functions and B‐type natriuretic peptide levels by cardiopulmonary exercise test in patients with pulmonary regurgitation after repair of tetralogy of fallot. J Card Surg， 2008， 5：493-498.
- 12. Eom J. Prenatal diagnosis and outcome of congenital absent pulmonaryvalve syndrome associated with tetralogy of Fallot：report of two cases. J Ultrasound Med， 2010， （S1）：174.
- 13. Yamamoto T， Dowa Y， Ueda H， et al. Tetralogy of fallot associated with pulmonary atresia and major aortopulmonary collateral arteriesin a patient with interstitial deletion of 16q21-q22.1. Am J Med Genet A， 2008， 146A （12）：1575-1580.
- 14. Horton RP， Canby RC， Kessler DJ， et al. Ablation of ventricular tachycardia associated with tetralogy of Fallot：demonstration of bidirectional block. J Cardiovasc Electrophysiol， 1997， 8 （4）：432-435.
- 15. Russo G， Folino AF， Mazzotti E， et al. Comparison between QRS duration at standard ECG and signal-averaging ECG for arrhythmicrisk stratification after surgical repair of tetralogy of fallot. JCardiovasc Electrophysiol， 2005， 16 （3）：288-292.
