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find Keyword "海马硬化" 15 results
  • 超极化激活环核苷酸门控通道在颞叶癫痫的研究新进展

    超极化激活环核苷酸门控通道(Hyperpolarizationactivated cyclic nucleotide gatedchannel,HCN)属于电压门控型离子通道,迄今为止发现有四个亚型:HCN1~HCN4。HCN 通道的激活依赖于膜的超级化,在膜电位低于静息电位时,HCN 通道被激活,产生局部紧张性电流,导致持续的钠内流,使细胞膜发生去极化。该通道分布在人体的分布并不一致,主要在神经系统和心脏中表达。目前研究表明,HCN 通道既参与所在组织的正常生理功能,如睡眠和觉醒、学习和记忆、视觉和疼痛感知、神经元起搏、树突整合等,也与多种中枢神经系统疾病及所在组织的病理状态密切相关,如神经病理性疼痛、学习记忆障碍、药物成瘾和颞叶癫痫,特别是在伴海马硬化性内侧颞叶癫痫中。癫痫作为神经系统最常见的神经疾病之一,癫痫因其病因错综复杂,病理改变亦多样性,至今尚未能完全了解其全部发病机制。目前有大量的文献报道 HCN 与癫痫,特别是颞叶癫痫的发生发展有密切关系。因此本文就 HCN 通道的结构特征、分布、功能、调控及其在颞叶癫痫发生过程中的新研究进展进行综述。

    Release date:2020-03-20 08:06 Export PDF Favorites Scan
  • 基于红藻氨酸和劳拉西泮联合给药的新型人类获得性颞叶癫痫动物模型

    红藻氨酸(Kainic acid,KA)是一种有效的谷氨酸类似物,用于诱导啮齿动物的神经退行性变和颞叶癫痫(TLE)。KA 可诱发严重的、持续的癫痫发作,即惊厥性癫痫持续状态(convulsive Status epilepticus,cSE),没有药物干预的情况下通常是致命的。在过去 30 年里,使用 KA 来建立人类癫痫动物模型毫无疑问被证明是有价值的,但显著的可变性和死亡率一直使结果变得不确定。这些问题很可能是 cSE 导致的,这是一种本质上可变且无法控制的全或无反应。然而,cSE 与人类疾病的相关性尚不确定,因为大多数癫痫患者从未经历过这种情况。该研究试图构建一种简单的、基于 KA 的 TLE 动物模型,以避免 cSE 及其混淆因素。成年雄性 Sprague-Dawley 大鼠分别接受皮下注射 KA(5 mg)和劳拉西泮(0.25 mg),剂量分别约为 15.0 mg/kg 和 0.75 mg/kg。持续的视频脑电图(VEEG)被用来监测急性癫痫的发作和检测自发性癫痫发作。免疫细胞化学、Fluoro-Jade B 染色和 Timm 染色被用来描述急性和慢性神经病理学改变。急性局灶海马癫痫发作在约 30 min 后开始并在几小时后自行终止。广泛的海马神经变性在 4 d 之后发现。在所有动物中自发性的局灶海马癫痫发作平均 12 d 之后开始。典型的海马硬化和苔藓纤维出芽的形成是长期神经病理学的特征。发病率和死亡率均为 0%。我们发现在联合注射低剂量苯二氮卓类药物时,KA 全身性给药的作用可局限于海马。这意味着劳拉西泮可以阻止痉挛性癫痫发作,而没有真正阻止癫痫电活动。这个创新的、无 cSE 的动物模型,可靠地模拟了获得性颞叶内侧癫痫所定义的特征:海马硬化和在长时间无癫痫发作后自发的海马起源的癫痫发作,并不伴显著的发病率、死亡率或无反应者。

    Release date:2019-03-21 11:04 Export PDF Favorites Scan
  • The clinic and Magnetic resonance imaging diagnostic in patients with temporal lobe epilepsy by hippocampal sclerosis

    ObjectiveThe research goal: to study the diagnostic value of T2-flair sequence of magnetic resonance imaging (MRI) in hippocampal sclerosis. MethodsThe clinical data of 135 patients with epilepsy caused by hippocampal sclerosis in the Epilepsy Center of Tianshui Third People's Hospital from March 2019 to December 2020 were analyzed retrospectively, studying the correlation between the changes of hippocampal sclerosis signal and the frequency of epileptic seizures in MRI T2-flair sequence multi axial scanning. ResultsThere were 109 cases of simple hippocampal sclerosis and 26 cases of hippocampal sclerosis with other lesions, including 8 cases of cavernous hemangioma, 9 cases of traumatic or infectious malacia, 2 cases of focal cortical dysplasia, 1 case of cerebral fissure malformation, 1 case of giant gyrus and 5 cases of perinatal brain injury. MRI features of hippocampal sclerosis were as follows: ① hippocampal volume increased slightly, structure blurred, and T2-flair showed slightly increased hippocampal signal in 15 cases, accounting for 11.11%; ② The hippocampal formation was fuzzy, T2-flair was punctate hyperintense, and the volume did not change in 17 cases (12.59%); ③ Hippocampal pyknosis into small lumps, T2-flair sequence showed high signal in 103 cases, accounting for 76.30%. Statistics showed that there was a correlation between hippocampal sclerosis signal and seizure frequency (χ2=94.94, P<0.05). The higher the hippocampal sclerosis signal, the more the seizure frequency. ConclusionMRI T2-flair sequence multi axial scanning can improve the diagnostic accuracy of hippocampal sclerosis. As the change of hippocampal sclerosis signal becomes more obvious, the trend of seizure frequency increases.

    Release date:2022-09-06 03:50 Export PDF Favorites Scan
  • 良性内侧颞叶癫痫的研究进展

    颞叶癫痫(TLE)是指异常过度放电起源于一侧或双侧颞叶结构的癫痫,是最常见的成人局灶性癫痫,也是最常见的药物难治性癫痫。内侧(Mesial)TLE 是 TLE 的主要类型,手术切除致痫灶是有效治疗方法。然而,部分患者的症状则较轻,并且能够在服用或未服用抗癫痫药物治疗的情况下达到无限期的缓解期,被认为是良性(benign)MTLE,此类患者经常有发热发作和癫痫的家族史。目前研究者认为 MTLE 可能与海马硬化和遗传因素有关,文章就 bMTLE 的研究进展进行总结,以提高临床对其认识。

    Release date:2019-01-19 08:54 Export PDF Favorites Scan
  • Analysis of 24 cases of intractable temporal lobe epilepsy surgery

    ObjectiveTo investigate the status and prognosis effect of surgical operation for Temporal lobe epilepsy.MethodsRetrospective analyses were performed on 24 patients with intractable temporal lobe epilepsy who were treated by surgery in Zibo Changguo Hospital and had complete clinical and follow-up data, during the period from April 2011 to June 2014. Among them, 14 were male and 10 were female, 16 to 44 years old, the average age was (24.40±6.26) years old, and the average course of disease was (12.50±8.42) years old. The clinical characteristics and prognosis of the patients were analyzed.ResultsAll 24 patients had hippocampal sclerosis and underwent "anterior temporal lobe and medial temporal structural resection". Patients were followed up for 5~7 years, the postoperative epileptic seizure of the patient reached grade Engel Ⅰ in 20 cases (83.3%), grade Engel Ⅱ in 2 cases (8.3%) and grade Engel Ⅳ in 2 cases (8.3%).ConclusionHippocampal sclerosis and cortical dysplasia were common in 24 patients, and the operation controlling intractable epilepsy was better. In order to improve the prognosis of patients, surgical treatment should be carried out as soon as possible.

    Release date:2021-02-27 02:57 Export PDF Favorites Scan
  • 1型神经纤维瘤病伴海马硬化及局灶性皮质发育不良癫痫手术治疗一例

    Release date:2024-11-20 10:50 Export PDF Favorites Scan
  • Progress in the study of the correlation between febrile convulsions and refractory epilepsy

    Febrile seizures (FS) are one of the most common neurological disorders in pediatrics, commonly seen in children from three months to five years of age. Most children with FS have a good prognosis, but some febrile convulsions progress to refractory epilepsy (RE). Epilepsy is a common chronic neurological disorder , and refractory epilepsy accounts for approximately one-third of epilepsies. The etiology of refractory epilepsy is currently complex and diverse, and its mechanisms are not fully understood. There are many pathophysiological changes that occur after febrile convulsions, such as inflammatory responses, changes in the blood-brain barrier, and oxidative stress, which can subsequently potentially lead to refractory epilepsy, and inflammation is always in tandem with all physiological changes as the main response. This article focuses on the pathogenesis of refractory epilepsy resulting from post-febrile convulsions.

    Release date:2023-09-07 11:00 Export PDF Favorites Scan
  • Altered spontaneous brain activity in mesial temporal lobe epilepsy with unilateral hippocampal sclerosis: a meta-analysis of resting-state functional magnetic resonance imaging

    Objective To identify the most consistent and replicable characteristics of altered spontaneous brain activity in mesial temporal lobe epilepsy patients with unilateral hippocampal sclerosis (MTLE-HS). Methods A systematic literature search was performed in PubMed, Embase, The Cochrane Library, China National Knowledge Infrastructure, Wanfang, and CQVIP databases, to identify eligible whole-brain resting state functional magnetic resonance imaging studies that had measured differences in amplitude of low-frequency fluctuations or fractional amplitude of low-frequency fluctuations between patients with MTLE-HS and healthy controls from January 2000 to January 2019. After literature screening and data extraction, Anisotropic Effect-Size Signed Differential Mapping software was used for voxel based pooled meta-analysis. Results Nine datasets from six studies were finally included, which contained 207 MTLE-HS patients and 239 healthy controls. The results demonstrated that, compared with the healthy controls, the MTLE-HS patients showed increased spontaneous brain activity in right hippocampus and parahippocampal gyrus, right superior temporal gyrus, left cingulate gyrus, right fusiform gyrus, and right inferior temporal gyrus; while decreased spontaneous brain activity in left superior frontal gyrus, right angular gyrus, right middle frontal gyrus, left inferior parietal lobule, left precuneus, and right cerebellum (P<0.005, cluster extent≥10). Conclusion The current meta-analysis demonstrates that patients with MTLE-HS show increased spontaneous brain activity in lateral and mesial temporal regions and decreased spontaneous brain activity in default mode network, which preliminarily clarifies the characteristics of altered spontaneous brain activity in patients with MTLE-HS.

    Release date:2019-11-25 04:42 Export PDF Favorites Scan
  • 海马硬化相关的颞叶癫痫的短期和长期手术预后:与神经病理学的关系

    海马硬化(Hippocampal sclerosis, HS)是接受手术治疗的难治性颞叶癫痫(Temporal lobe epilepsy, TLE)患者中最常见的病理类型。国际抗癫痫联盟(ILAE)最近按细胞丢失的不同类型提出一个新的HS分类。研究旨在探讨HS不同类型之间的关系、病因、有HS的耐药性TLE患者术后短期及长期预后。213例术后病理诊断为HS的患者纳入此研究,每例至少随访2年时间。患者依照ILAE标准进行HS分类,并进一步分为单纯HS(Isolated HS, IHS)、HS伴皮质发育不良(Focal cortical dysplasia, FCD IIIa)和HS伴其他病灶。将患者临床及病理特点与其以标准来评价的术后预后进行对比。主要发现如下:① 1型HS癫痫病程较长;② 80%以上患者短期和长期预后均在EngelⅠ级,无论何种HS类型和相关病理学改变;③短期和长期的术后预后在完全无癫痫发作的患者(EngelⅠa级)中较不令人满意,2型HS患者长期预后较1型更好;④无论HS为何种类型,伴有FCD的患者预后较差;⑤较短的癫痫持续时间与EngelⅠa级预后有显著关联。研究结果表明HS类型与相关病理改变能预测术后复发风险的重要因素,而其他变量如癫痫持续时间也需要考虑。公认的神经病理学分类标准有助于识别术前预测因素,并有助于筛选可能从癫痫手术中获益的患者。

    Release date:2017-11-27 02:36 Export PDF Favorites Scan
  • Surgical treatment for the temporal lobe epilepsy with hippocampal sclerosis: report of 42 cases

    ObjectiveTo explore the clinical features and surgical treatment effects of the temporal lobe epilepsy with hippocampal sclerosis.MethodsForty two patients diagnosed as temporal lobe epilepsy with hippocampal sclerosis and underwent protemporal lobectomy in Wuhan Brain Hospital from Jan. 2012 to Dec. 2018 were collected, which included 30 males and 12 females, with the age between 9 to 60 years. Their disease duration ranged from 3 to 10 years. The clinical manifestations showed complex partial seizure in 18 cases, partial-secondary –generalized seizure in 4 cases, and generalized tonic-clonic seizure in 20 cases. Based on their results of clinical manifestations, combined with MRI and VEEG results, all the patients underwent anterior temporal lobectomy (including the most parts of the hippocampus and amydala).ResultsThe postoperative pathology confirmed the diagnosis of hippocampal sclerosis. The follow-up of more than 1 year showed seizure-free in 38 cases, and significant improvement in 4 cases.ConclusionsTo the patients of temporal lobe epilepsy with hippocampal sclerosis, anterior temporal lobectomy should be performed (including the most parts of the hippocampus and amydala) if the VEEG monitoring results show that there are epileptic discharges in the ipsilateral temporal lobe. And the postoperative curative result is satisfactory.

    Release date:2019-05-21 08:51 Export PDF Favorites Scan
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